IgG4-Related Pericarditis

IgG4-RD pericarditis is a rare but important cause of constrictive physiology. Multimodality imaging and pericardial biopsy are critical for diagnosis. Surgical pericardiectomy is often curative, but lifelong follow-up is necessary to monitor systemic disease.

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Publication Details

Journal
JACC Case Reports
Published
2026-01-27
DOI
https://doi.org/10.1016/j.jaccas.2026.106859
Primary Topic
IgG4-Related and Inflammatory Diseases
Type
article
Field-Weighted Citation Impact
0.00
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article

IgG4-Related Pericarditis

Chadi Tabaja, Joseph El Roumi, Tom Wang, Faysal Massad et al.
JACC Case Reports
IgG4-Related and Inflammatory Diseases
article

IgG4-Related Pericarditis

Chadi Tabaja, Joseph El Roumi, Tom Wang, Faysal Massad, Vaidehi Mendpara, Muhammad Ehsan, Allan Klein, Jibran Ikram, Michael Villalonga, Marc K. Halushka
article en

Abstract

IgG4-RD pericarditis is a rare but important cause of constrictive physiology. Multimodality imaging and pericardial biopsy are critical for diagnosis. Surgical pericardiectomy is often curative, but lifelong follow-up is necessary to monitor systemic disease.

JACC Case ReportsVol. 31(10)
Cleveland Clinic (US), Cleveland Clinic Lerner College of Medicine (US)
Openalex Percentile: Top 78%
IgG4-Related and Inflammatory Diseases
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