Paediatric caecal volvulus, a rare presentation of african degenerative leiomyopathy – a case report

ADL is a rare and often fatal condition associated with intermittent bowel obstruction and systemic complications, including cardiac and urologic abnormalities. In paediatric patients, caecal volvulus should prompt consideration of PIPO as an underlying diagnosis.

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Publication Details

Journal
International Journal of Colorectal Disease
Published
2026-01-26
DOI
https://doi.org/10.1007/s00384-026-05093-y
Primary Topic
Intestinal Malrotation and Obstruction Disorders
Type
article
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article

Paediatric caecal volvulus, a rare presentation of african degenerative leiomyopathy – a case report

Francesca Palmisani, Seo-Hwa Chung, Giulia Brisighelli, Emanuele Trovalusci et al.
International Journal of Colorectal Disease
Intestinal Malrotation and Obstruction Disorders
article

Paediatric caecal volvulus, a rare presentation of african degenerative leiomyopathy – a case report

Francesca Palmisani, Seo-Hwa Chung, Giulia Brisighelli, Emanuele Trovalusci, Sphamandla Zulu, Leila Hartford
article en

Abstract

ADL is a rare and often fatal condition associated with intermittent bowel obstruction and systemic complications, including cardiac and urologic abnormalities. In paediatric patients, caecal volvulus should prompt consideration of PIPO as an underlying diagnosis.

International Journal of Colorectal DiseaseVol. 41(1)
University of Padua (IT), Chris Hani Baragwanath Hospital (ZA), Medical University of Vienna (AT)
No poverty
Openalex Percentile: Top 77%
Intestinal Malrotation and Obstruction Disorders
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