Current treatment decisions in cardiac transthyretin amyloidosis: a multicentre analysis

In this multicentre analysis, treatment with tafamidis was initiated in about 80% of patients with newly diagnosed ATTR-CM. In most centres, treatment decisions were made by an interdisciplinary board, and the reasons for treatment decisions were similar across centres. Due to the lack of consensus criteria, our data may help to standardise decision pathways for ATTR-CM.

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Publication Details

Journal
Clinical Research in Cardiology
Published
2026-01-26
DOI
https://doi.org/10.1007/s00392-026-02848-z
Primary Topic
Amyloidosis: Diagnosis, Treatment, Outcomes
Type
article
Field-Weighted Citation Impact
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article

Current treatment decisions in cardiac transthyretin amyloidosis: a multicentre analysis

Christian Nagel, Roman Pfister, Maximilian Steinhardt, Ingrid Kindermann et al.
Clinical Research in Cardiology
Amyloidosis: Diagnosis, Treatment, Outcomes
article

Current treatment decisions in cardiac transthyretin amyloidosis: a multicentre analysis

Christian Nagel, Roman Pfister, Maximilian Steinhardt, Ingrid Kindermann, Julia Vogel, Sebastian Spethmann, Stefanie Jellinghaus, Gina Barzen, Teresa Trenkwalder, Lisa Schöner, Yavor Metodiev, Matthieu Schäfer, Stéphanie Kristina Schwarting, Eva Hofmann, Bernhard W. Unsöld, Dominik Kauffmann, Aikaterini Papagianni, Katrin Hahn, Julian Mustroph, Daniel Lavall, K. Knoll, Alexandru Zlibut, Monique Tröbs, C Morbach, Lara Schlender, Ali Yilmaz, Stefan T. Störk, Natascha Majunke, A. Zimmer, Thomas Krammer, Lars Michel, Birgit Aßmus, Maria Papathanasiou, David M. Leistner, Fabian aus dem Siepen, Maria Tafelmeier, Irina Müller-Kozarez, Heribert Schunkert, Larissa Bühner, Tienush Rassaf, Selen Alieva, Nora Donhauser, Ephraim B. Winzer, Patrick Fuchs, Vladimir Cejka
article en

Abstract

In this multicentre analysis, treatment with tafamidis was initiated in about 80% of patients with newly diagnosed ATTR-CM. In most centres, treatment decisions were made by an interdisciplinary board, and the reasons for treatment decisions were similar across centres. Due to the lack of consensus criteria, our data may help to standardise decision pathways for ATTR-CM.

Clinical Research in Cardiology
Goethe University Frankfurt (DE), Friedrich-Alexander-Universität Erlangen-Nürnberg (DE), Justus-Liebig-Universität Gießen (DE), Heidelberg University (DE), University Hospital Heidelberg (DE), LMU Klinikum (DE), University Hospital Regensburg (DE), Humboldt-Universität zu Berlin (DE), University Hospital Münster (DE), Deutsches Herzzentrum der Charité (DE), University Hospital Leipzig (DE), Universitätsklinikum Würzburg (DE), German Centre for Cardiovascular Research (DE), University Hospital Frankfurt (DE), Berlin Institute of Health at Charité - Universitätsmedizin Berlin (DE), Deutsches Herzzentrum München (DE), University Hospital Cologne (DE), West German Heart and Vascular Center Essen (DE), Technical University of Munich (DE), Technische Universität Dresden (DE), Charité - Universitätsmedizin Berlin (DE), Ludwig-Maximilians-Universität München (DE), Saarland University (DE), Leipzig University (DE)
Peace, Justice and strong institutions
Openalex Percentile: Top 78%
Amyloidosis: Diagnosis, Treatment, Outcomes
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