VEXAS syndrome and cancer: Insights about a possible “Tip of the Iceberg”. Ambidirectional data from the international AIDA network registries

VEXAS patients exhibit a significantly increased risk of both hematologic and non-hematologic malignancies compared with controls, particularly among those with RP, p.Met41Thr mutation, and persistent systemic inflammation.

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Publication Details

Journal
Seminars in Arthritis and Rheumatism
Published
2026-01-22
DOI
https://doi.org/10.1016/j.semarthrit.2026.152932
Primary Topic
Otitis Media and Relapsing Polychondritis
Type
article
Field-Weighted Citation Impact
0.00
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article

VEXAS syndrome and cancer: Insights about a possible “Tip of the Iceberg”. Ambidirectional data from the international AIDA network registries

F. Conti, A. Floris, Vito Racanelli, Guillermo Arturo Guaracha-Basáñez et al.
Seminars in Arthritis and Rheumatism
Otitis Media and Relapsing Polychondritis
article

VEXAS syndrome and cancer: Insights about a possible “Tip of the Iceberg”. Ambidirectional data from the international AIDA network registries

F. Conti, A. Floris, Vito Racanelli, Guillermo Arturo Guaracha-Basáñez, Amato de Paulis, C. Fabiani, Valeria Caggiano, Antonio Vitale, L. Cantarini, Francesca Crisafulli, Alberto Balistreri, Monica Bocchia, Alessandra Milanesi, Adriana Soto-Peleteiro, M. Frassi, Juan José Alegre Sancho, Carmelo Gurnari, B. Frediani, Alberto Alemanno, Chiara Cardamone, Lorenzo DAGNA, Anna Sicuranza, Francesco Gavioli, Mark Beecher, Pravin Hissaria, A. Mayo-Juanatey, Matteo Piga, Jessica Sbalchiero, Büsra Köksoy, Marta Schermi, Henrique A. Mayrink Giardini, Paolo Sfriso, Sara Bindoli, Serena Bugatti, Jiram Torres-Ruiz, Rosetta Vitetta, Thomas Panayiaris, Francesco Placido, José Hernández-Rodríguez, Fatih Mulayim, Ombretta Viapiana, Verónica Gómez-Caverzaschi, Francesca Silvan, Alberto Cauli, Marcella Prete, Paola Triggianese, Ilaria Zorzenon, Vincenzo Sorrentino, Alessandra Renieri, Elisa Frullanti, Abdurrahman Tufan, Rosaria Talarico, Olga Araújo, Andrés González-García, Ilaria Cavazzana, Corrado Campochiaro, Giuseppe Lopalco, Guillermo Ruiz-Irastorza, Samuele Rizzo
article en

Abstract

VEXAS patients exhibit a significantly increased risk of both hematologic and non-hematologic malignancies compared with controls, particularly among those with RP, p.Met41Thr mutation, and persistent systemic inflammation.

Seminars in Arthritis and RheumatismVol. 77
University of Siena (IT), University of Pisa (IT), University of Rome Tor Vergata (IT), Cleveland Clinic (US), Royal Adelaide Hospital (AU), University of Padua (IT), Vita-Salute San Raffaele University (IT), University of Cagliari (IT), University of Trento (IT), Policlinico Umberto I (IT), Ospedale Santa Chiara (IT), BioCruces Health research Institute (ES), Azienda Ospedaliera Universitaria Integrata Verona (IT), Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán (MX), CTO Andrea Alesini (IT), Federico II University Hospital (IT), Siena Biotech (Italy) (IT), Wojskowy Instytut Medycyny Lotniczej (PL), Hospital Universitario Doctor Peset (ES), Instituto Ramón y Cajal de Investigación Sanitaria (ES), IRCCS Ospedale San Raffaele (IT), Ospedali Riuniti San Giovanni di Dio e Ruggi d'Aragona (IT), Azienda Ospedaliera Universitaria Senese (IT), Policlinico Tor Vergata (IT), Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (BR), Policlinico San Matteo Fondazione (IT), Consorci Institut D'Investigacions Biomediques August Pi I Sunyer (ES), Hospital Universitario Ramón y Cajal (ES), University of Bari Aldo Moro (IT), University of Naples Federico II (IT), Universitat de Barcelona (ES), University of Brescia (IT), Gazi University (TR)
Good health and well-being
Openalex Percentile: Top 82%
Otitis Media and Relapsing Polychondritis
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