Human Plasma‐Derived <scp>C1</scp> Inhibitor for Short‐Term Prophylaxis in Hereditary Angioedema With Normal <scp>C1</scp> Inhibitor

Summary STP with plasma‐derived C1 inhibitor in patients with HAE‐nC1INH can reduce the risk of post‐procedure attacks. Efficacy in preventing attacks in patients with HAE‐FXII was higher than in those with HAE‐UNK.

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Publication Details

Journal
Clinical & Experimental Allergy
Published
2026-01-20
DOI
https://doi.org/10.1111/cea.70218
Primary Topic
Coagulation, Bradykinin, Polyphosphates, and Angioedema
Type
article
Field-Weighted Citation Impact
0.00
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article

Human Plasma‐Derived C1 Inhibitor for Short‐Term Prophylaxis in Hereditary Angioedema With Normal C1 Inhibitor

Eli Mansour, Rozana de Fátima Gonçalves, Janáira Fernandes Severo Ferreira, Iramirton Figuerêdo Moreira et al.
Clinical & Experimental Allergy
Coagulation, Bradykinin, Polyphosphates, and Angioedema
article

Human Plasma‐Derived C1 Inhibitor for Short‐Term Prophylaxis in Hereditary Angioedema With Normal C1 Inhibitor

Eli Mansour, Rozana de Fátima Gonçalves, Janáira Fernandes Severo Ferreira, Iramirton Figuerêdo Moreira, Mariana Paes Leme Ferriani, J. L. R. Lemos, Luís Felipe Ramos Berbel Angulski, Gabriela Andrade Coelho Dias, Herberto José Chong Neto, Jane Silva, Clarissa Lucia Tenório Soares Vieira Tavares, Anete S. Grumach, Paula Christina Cavallini de Melo Maricondi, Fernanda Gontijo Minafra, Solange Oliveira Rodrigues Valle, Maria Luiza Oliva‐Alonso, Faradiba Sarquis Serpa, L. Karla Arruda, Adriana Azoubel‐Antunes
article en

Abstract

Summary STP with plasma‐derived C1 inhibitor in patients with HAE‐nC1INH can reduce the risk of post‐procedure attacks. Efficacy in preventing attacks in patients with HAE‐FXII was higher than in those with HAE‐UNK.

Clinical & Experimental Allergy
Universidade Federal de Minas Gerais (BR), Universidade Federal do Rio de Janeiro (BR), Universidade Federal da Bahia (BR), Universidade de Ribeirão Preto (BR), Universidade Estadual de Campinas (UNICAMP) (BR), Universidade Federal de Pernambuco (BR), Universidade do Estado do Rio de Janeiro (BR), Universidade Sagrado Coração (BR), Escola Superior de Ciências da Santa Casa de Misericórdia de Vitória (BR), Polydoro Ernani de São Thiago University Hospital (BR), Centro Universitário Cesmac (BR), Hospital Infantil Albert Sabin (BR), Faculdade de Medicina do ABC (BR), Clinics Hospital of Ribeirão Preto (BR), Universidade Federal do Paraná (BR)
Openalex Percentile: Top 82%
Coagulation, Bradykinin, Polyphosphates, and Angioedema
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