A case of prune belly syndrome with patent urachus: Pediatric surgical aspects of a rare case report

Prune belly syndrome (PBS), or Eagle-Barrett syndrome, is a rare congenital disorder defined by a triad of abdominal wall hypoplasia, urinary tract anomalies, and bilateral cryptorchidism. It is associated with high perinatal morbidity and mortality. A male infant born at 37 weeks via vaginal delivery presented with abdominal distension, thin wrinkled abdominal skin, urine discharge from the umbilicus, and bilateral cryptorchidism. Imaging revealed severe bilateral hydronephrosis and a patent urachus, confirming Prune Belly Syndrome. The urachus was surgically closed without complications, and the patient remains stable, with planned further interventions including orchidopexy, abdominal wall reconstruction, and renal functional assessment. Prune Belly Syndrome a rare congenital disorder, presents diagnostic and management challenges particularly with patent urachus requiring early recognition, timely surgery, and multidisciplinary follow-up to optimize renal function and long-term outcomes.