Incidence and predictors of self-reported pulmonary exacerbations in primary ciliary dyskinesia: an international prospective cohort study
Pulmonary exacerbations are frequent in PCD and heighten the disease burden. Patients for whom targeted management is particularly important include adult females and those who carry <i>P. aeruginosa</i>.
Authors
- Leonie D Schreck (ORCID: https://orcid.org/0000-0001-6180-692X)
- Jane S. Lucas (ORCID: https://orcid.org/0000-0001-8701-9975)
- E. S. L. Pedersen
- Fiona Copeland
- Myrofora Goutaki
- Living with PCD patient advisory group
- Trini López Fernández
- Claudia E. Kuehni
Institutions
- University of Bern (CH)
- University Hospital of Bern (CH)
- University Hospital Southampton NHS Foundation Trust (GB)
- Institute of Social and Preventive Medicine (CH)
- University of Southampton (GB)
- Universidad de Murcia (ES)
Publication Details
- Journal
- ERJ Open Research
- Published
- 2025-08-14
- DOI
- https://doi.org/10.1183/23120541.00686-2025
- Primary Topic
- Cystic Fibrosis Research Advances
- Type
- article
- Field-Weighted Citation Impact
- 0.00