Clinical and laboratory markers to distinguish VEXAS from Schnitzler's syndrome: data from the AIDA network registries

Patients with lymphadenopathy, thrombocytopenia, anemia, particularly in older age and in the absence of leucocytosis, are more likely to be affected by VEXAS syndrome rather than Schnitzler's syndrome.

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Publication Details

Journal
Frontiers in Medicine
Published
2026-01-12
DOI
https://doi.org/10.3389/fmed.2025.1659758
Primary Topic
Otitis Media and Relapsing Polychondritis
Type
article
Field-Weighted Citation Impact
0.00

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article

Clinical and laboratory markers to distinguish VEXAS from Schnitzler's syndrome: data from the AIDA network registries

F. Conti, Andreas Recke, Gaafar Ragab, Fernando Tornero-Romero et al.
Frontiers in Medicine
Otitis Media and Relapsing Polychondritis
article

Clinical and laboratory markers to distinguish VEXAS from Schnitzler's syndrome: data from the AIDA network registries

F. Conti, Andreas Recke, Gaafar Ragab, Fernando Tornero-Romero, Marcin Ziętkiewicz, Leyla La Cava, Paolo Moscato, Guillermo Arturo Guaracha-Basáñez, Amato de Paulis, G. Ruiz-Irastorza, C. Fabiani, Valeria Caggiano, Antonio Vitale, Ombretta Viapiana, Chiara Baggio, L. Cantarini, G. Espinosa, Francesca Crisafulli, Alberto Balistreri, Monica Bocchia, Alessandra Milanesi, C. Campochiaro, Karina Jahnz‐Różyk, M. Frassi, P. Triggianese, Carmelo Gurnari, B. Frediani, C. Chighizola, G. Lopalco, Lorenzo DAGNA, Anna Sicuranza, Antonio Gidaro, Mark Beecher, Ilaria Mormile, Paolo Airò, Pravin Hissaria, Rafael Alves Cordeiro, M. Prete, A. González-García, Mercedes Peña Rodríguez, Giacomo Emmi, Matteo Piga, Jessica Sbalchiero, Florenzo Iannone, Perla Ayumi Kawakami-Campos, Henrique A. Mayrink Giardini, Abdurrahman Tufan, Hamit Kucuk, Paolo Sfriso, Mariusz Sikora, Sara Bindoli, Verónica Gómez Caverzaschi, José Hernández-Rodríguez, Serena Bugatti, Jiram Torres-Ruiz, Rosetta Vitetta
article en

Abstract

Patients with lymphadenopathy, thrombocytopenia, anemia, particularly in older age and in the absence of leucocytosis, are more likely to be affected by VEXAS syndrome rather than Schnitzler's syndrome.

Frontiers in MedicineVol. 12
University of Siena (IT), South Australia Pathology (AU), University of Rome Tor Vergata (IT), Cleveland Clinic (US), Royal Adelaide Hospital (AU), University of Padua (IT), University of Trieste (IT), Cairo University (EG), Vita-Salute San Raffaele University (IT), Carol Davila University of Medicine and Pharmacy (RO), University of the Basque Country (ES), University of Cagliari (IT), University of Milan (IT), University of Ferrara (IT), University of Pavia (IT), Policlinico Umberto I (IT), Monash Medical Centre (AU), Luigi Sacco Hospital (IT), BioCruces Health research Institute (ES), Azienda Ospedaliera Universitaria Integrata Verona (IT), Ospedale di Cattinara (IT), Instituto Nacional de Ciencias Médicas y Nutrición Salvador Zubirán (MX), Euroimmun Medizinische Labordiagnostika (Germany) (DE), University Hospital Schleswig-Holstein (DE), CTO Andrea Alesini (IT), Wojskowy Instytut Medycyny Lotniczej (PL), Instituto Ramón y Cajal de Investigación Sanitaria (ES), Hospital Universitario Fundación Jiménez Díaz (ES), IRCCS Ospedale San Raffaele (IT), Ospedali Riuniti San Giovanni di Dio e Ruggi d'Aragona (IT), Azienda Ospedaliera Universitaria Senese (IT), Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (BR), Consorci Institut D'Investigacions Biomediques August Pi I Sunyer (ES), Hospital Universitario Ramón y Cajal (ES), University of Bari Aldo Moro (IT), Monash University (AU), University of Naples Federico II (IT), Universitat de Barcelona (ES), Gdańsk Medical University (PL), University of Brescia (IT), University of Lübeck (DE), Gazi University (TR)
Università degli Studi di Padova, Università degli Studi di Pavia, Università degli Studi di Brescia
Openalex Percentile: Top 92%
Otitis Media and Relapsing Polychondritis
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