Painful subcutaneous edema is associated with early age at disease onset in Immunoglobulin A vasculitis patients: A multicenter study
PSE occurred in approximately one-third-of IgAV patients at disease onset and was diagnosed predominantly at an early age, with a more inflammatory presentation at onset. However, in spite of the higher levels of inflammatory markers, PSE was not linked to more severe outcomes.
Authors
- Paula Santana Marra
- Lia Vineyard Steuer (ORCID: https://orcid.org/0000-0002-0828-1949)
- Cláudio Arnaldo Len (ORCID: https://orcid.org/0000-0001-8636-1744)
- Clovis AA Silva
- Vitória Zampieri Curi
- Lucia MA Campos
- Virginia PL Ferriani
- Clara Ribeiro Doria
- Adriana Maluf Elias
- Matheus Santos França
- Sebastian D. Cordoba
- Gleice Clemente
- Verena A. Balbi
- Flavio R. Sztajnbok
- Ricardo N. Machado
- Sylvia C.L. Farhat
- Francisco H.R. Gomes
- Beatriz O.L. Carneiro
- Katia T. Kozu
- Luciana M. Carvalho
- Luisa F.C. Forero
- Rozana G. de Almeida
- Magda Carneiro-Sampaio
- Nadia E. Aikawa
Institutions
- Universidade Federal do Rio de Janeiro (BR)
- Universidade de Ribeirão Preto (BR)
- Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (BR)
- Universidade Federal de São Paulo (BR)
Publication Details
- Journal
- Clinics
- Published
- 2026-01-01
- DOI
- https://doi.org/10.1016/j.clinsp.2025.100857
- Primary Topic
- Vasculitis and related conditions
- Type
- article
- Field-Weighted Citation Impact
- 0.00