Gamma heavy-chain disease presenting with hypercalcaemia and ascites
Consider gamma heavy-chain disease in patients with unexplained monoclonal gammopathy and atypical presentations, such as hypercalcaemia and ascites.A combination of rituximab and chemotherapy shows an anti-tumour effect in gamma heavy-chain disease expressing CD20.
Authors
- Pauline Lionne
- L. Terriou
- Imane El Boutahiri
- Kmar Mrad
Institutions
- Université de Lille (FR)
- Centre de Référence des Maladies Autoinflammatoires et des Amyloses (FR)
- Centre Hospitalier d'Arras (FR)
- Université Lille Nord de France (FR)
Publication Details
- Journal
- European Journal of Case Reports in Internal Medicine
- Published
- 2026-01-09
- DOI
- https://doi.org/10.12890/2026_005987
- Primary Topic
- Amyloidosis: Diagnosis, Treatment, Outcomes
- Type
- article
- Field-Weighted Citation Impact
- 0.00