Antineutrophil Cytoplasmic Antibody–Associated Vasculitides in Systemic Sclerosis: A Unique Clinical Overlap With Significant Implications for Treatment and Outcomes

AAV, predominantly microscopic polyangiitis with MPO-ANCA, can occur in SSc, particularly in patients with fibrosing ILD and anti-Scl70. Standard vasculitis treatments appear to be effective and do not worsen outcomes in SSc.

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Publication Details

Journal
Arthritis & Rheumatology
Published
2025-12-26
DOI
https://doi.org/10.1002/art.70032
Primary Topic
Systemic Sclerosis and Related Diseases
Type
article
Field-Weighted Citation Impact
0.00
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article

Antineutrophil Cytoplasmic Antibody–Associated Vasculitides in Systemic Sclerosis: A Unique Clinical Overlap With Significant Implications for Treatment and Outcomes

Alexandre Cez, Luc Mouthon, Carole Philipponnet, Noémie Jourde‐Chiche et al.
Arthritis & Rheumatology
Systemic Sclerosis and Related Diseases
article

Antineutrophil Cytoplasmic Antibody–Associated Vasculitides in Systemic Sclerosis: A Unique Clinical Overlap With Significant Implications for Treatment and Outcomes

Alexandre Cez, Luc Mouthon, Carole Philipponnet, Noémie Jourde‐Chiche, V. Audard, C. Durel, Stanislas Faguer, Nicolas Limal, B. Chaigne, Aurélie Lavergne, Christian Lavigne, Déborah Eshagh, A. Servettaz, Jean‐François Augusto, Théophile Hubsch, Alexandre Karras, P. Smets, Pierre Duffau, V. Queyrel, Marion Couderc, Alexis Régent, Rafik Mesbah, Benjamin Terrier, the French Vasculitis Study Group, Xavier Puéchal, Thomas Quéméneur, Christian Agard
article en

Abstract

AAV, predominantly microscopic polyangiitis with MPO-ANCA, can occur in SSc, particularly in patients with fibrosing ILD and anti-Scl70. Standard vasculitis treatments appear to be effective and do not worsen outcomes in SSc.

Arthritis & Rheumatology
Inserm (FR), Université Fédérale de Toulouse Midi-Pyrénées (FR), Université Paris-Est Créteil (FR), Centre Hospitalier Universitaire de Grenoble (FR), Centre Hospitalier Universitaire de Bordeaux (FR), Centre Hospitalier Universitaire de Nice (FR), Centre Hospitalier Universitaire de Nantes (FR), Centre Hospitalier Universitaire de Toulouse (FR), Sorbonne Université (FR), Sorbonne Paris Cité (FR), Hôpital Cochin (FR), Hôpital Européen Georges-Pompidou (FR), Centre Hospitalier Universitaire de Reims (FR), Centre Hospitalier Universitaire d'Angers (FR), Hôpital Edouard Herriot (FR), Centre Hospitalier Universitaire de Clermont-Ferrand (FR), Hôpitaux Universitaires Henri-Mondor (FR), Hôpital d'Instruction des Armées Sainte-Anne (FR), Centre Pompidou (FR), Université d'été de Boulogne-sur-Mer (FR), Centre Hospitalier Universitaire de Rennes (FR), Centre Hospitalier de Valenciennes (FR), Institut Mondor de Recherche Biomédicale (FR), Hôpital Tenon (FR), Université de Reims Champagne-Ardenne (FR)
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Openalex Percentile: Top 30%
Systemic Sclerosis and Related Diseases
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