Fatal familial insomnia with a Lewy‐like presentation
FFI can present with a heterogeneous phenotype. Patients with symptoms resembling DLB but showing alarm signs (rapid progressive dementia, multiple sleep abnormalities, strong family history) should prompt a more thorough investigation.
Authors
- Hindalis Ballesteros Epifanio
- Maurício Silva Teixeira
- Edson Bor‐Seng‐Shu
- Patrícia Faria Scherer
- Sônia Maria Dozzi Brucki (ORCID: https://orcid.org/0000-0002-8303-6732)
- Anna Maria Gomes
- Cícero José Nunes Vaz
Institutions
- Hospital Israelita Albert Einstein (BR)
- Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo (BR)
Publication Details
- Journal
- Alzheimer s & Dementia
- Published
- 2025-12-01
- DOI
- https://doi.org/10.1002/alz70857_102926
- Primary Topic
- Prion Diseases and Protein Misfolding
- Type
- article
- Field-Weighted Citation Impact
- 0.00