Clinical implications of Vasculitis associated with familial Mediterranean fever: a comparative study in childhood

The coexistence of vasculitis in FMF likely reflects shared inflammatory mechanisms rather than coincidence. Vasculitis occurred even in patients with milder MEFV genotypes, suggesting an enhanced proinflammatory milieu. Early recognition of vasculitis in FMF may influence therapeutic strategies and improve outcomes.

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Publication Details

Journal
Modern Rheumatology
Published
2025-12-23
DOI
https://doi.org/10.1093/mr/roaf128
Primary Topic
Inflammasome and immune disorders
Type
article
Field-Weighted Citation Impact
0.00
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article

Clinical implications of Vasculitis associated with familial Mediterranean fever: a comparative study in childhood

Ayşenur Doğru, Selen Duygu Arık, Özlem Martı Akgün, Nuray Aktay Ayaz et al.
Modern Rheumatology
Inflammasome and immune disorders
article

Clinical implications of Vasculitis associated with familial Mediterranean fever: a comparative study in childhood

Ayşenur Doğru, Selen Duygu Arık, Özlem Martı Akgün, Nuray Aktay Ayaz, Büşra Başer Taşkın
article en

Abstract

The coexistence of vasculitis in FMF likely reflects shared inflammatory mechanisms rather than coincidence. Vasculitis occurred even in patients with milder MEFV genotypes, suggesting an enhanced proinflammatory milieu. Early recognition of vasculitis in FMF may influence therapeutic strategies and improve outcomes.

Modern Rheumatology
Istanbul University (TR)
Openalex Percentile: Top 36%
Inflammasome and immune disorders
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