“The Eyes See Only What The Mind Knows”: Klippel-Trenaunay Syndrome with Multiple Intracranial Aneurysms

A bstract Klippel-Trenaunay syndrome (KTS) is a rare congenital condition characterized by cutaneous hemangiomas, varicosities, and hypertrophy of bone or soft tissue, resulting in limb asymmetry. We present a case involving a 13-year-old male who was admitted to Sri Ramachandra Medical College, Chennai, exhibiting headache, vomiting, and drowsiness for six days. A computed tomography (CT) scan indicated obstructive hydrocephalus and vertebrobasilar dolichoectasia. His Glasgow Coma Scale score fell to E2V2M4, necessitating emergency intubation. An urgent right ventriculoperitoneal (VP) shunt was performed, after which he was moved to the intensive care unit for support and antiepileptic medication. Postoperative CT imaging confirmed a well-positioned VP shunt, subarachnoid hemorrhage, and diminished ventricular size. The cardiac evaluation revealed cardiomyopathy with a reduced ejection fraction. Despite inotropic support, hemodynamic stabilization was not achieved. The patient experienced bradycardia and desaturation during resuscitation efforts, ultimately resulting in his death.