Management of Oral Health of Children with Encephalotrigeminal Angiomatosis

Sturge–Weber Syndrome (SWS) is an uncommon neurocutaneous condition present at birth, marked by facial port-wine stains (PWB), leptomeningeal vascular malformations, and eye-related problems. This report discusses two pediatric cases of SWS who presented to the department with dental pain as primary concern. Both patients exhibited facial PWB and oral manifestations, including gingival vascular malformations. Detailed clinical, radiographic, and medical assessments confirmed the diagnosis of SWS. Dental management involved preventive and restorative procedures such as oral prophylaxis, restorations, pulpectomy, stainless steel and strip crowns, and space maintainers, with emphasis on maintaining oral hygiene. These cases highlight the importance of early diagnosis, individualized dental care, and interdisciplinary collaboration in managing the oral and systemic manifestations of SWS. Regular follow-up and patient education played a critical role in successful management.