Cosmetic Rehabilitation in Congenital Cataract with Persistent Hyperplastic Primary Vitreous

A BSTRACT Persistent hyperplastic primary vitreous (PHPV), a rare congenital ocular anomaly resulting from halted regression of the fetal hyaloid vascular system. It typically presents with leukocoria and poor vision in infancy. A 11-year-old girl presenting with profound visual loss in the left eye necessitating ophthalmic evaluation. Clinical examination revealed a mature cataract in the left eye. Imaging confirmed the diagnosis of PHPV. Treatment included surgical intervention in which small incision cataract surgery with posterior chamber intraocular lens implantation was performed in the left eye primarily for cosmetic improvement. Despite meticulous intervention, visual recovery remained minimal. The case underscores the nuanced approach required in managing PHPV cases, balancing cosmetic concerns with realistic visual outcomes, thereby enriching the discourse on pediatric ophthalmic interventions. This case report highlights the challenges in achieving cosmesis in patients with congenital cataract and PHPV, emphasizing the importance of early intervention and comprehensive management strategies for optimal outcomes.