RUPTURED SINUS OF VALSALVA IN A NEONATE: CASE REPORT AND REVIEW OF LITERATURE

Sinus of Valsalva aneurysm (SVA) is an abnormal dilatation of one or more aortic sinuses located between the aortic valve annulus and the sinotubular junction. Rupture of SVA can lead to left-to-right shunting, most commonly into the right cardiac chambers. Although aortic sinus aneurysm rupture accounts for less than 1% of congenital cardiac lesions, its incidence varies by geography and population. Rupture of the sinus of Valsalva is a potentially fatal condition if not promptly diagnosed, and timely multidisciplinary management is essential for optimal outcomes. Rupture of the sinus of Valsalva (RSOV) into the right cardiac chambers represents an uncommon complication characterized by atypical presentation, distinctive hemodynamic alterations, and unique echocardiographic features. We are herein presenting a rare case of a 13-day-old neonate striken with severe respiratory distress. Color Doppler echocardiography revealed a characteristic rupture of the right coronary cusp of the aorta, accompanied by a moderately sized atrial septal defect (ASD), and significant pulmonary hypertension.