‘Storiform Story’ – A Case of Chronic Tubulointerstitial Nephritis due to Immunoglobulin G4-Related Disease

IgG4-related kidney disease (IgG4-RKD) is a rare cause of chronic tubulointerstitial nephritis (TIN), with limited reports from India. Its nonspecific presentation and overlapping lab findings make renal biopsy and immunohistochemistry essential for diagnosis. This case adds to the clinicopathologic spectrum, potentially aiding early recognition, guiding treatment, and contributing to understanding the disease’s epidemiology in the Indian context.