Full mouth rehabilitation of a pediatric patient with Sturge-weber syndrome under general Anaesthesia: A case report

Sturge-Weber syndrome (SWS) or encephalotrigeminal angiomatosis is a neurocutaneous typified by angiomas that affect the face, choroid, and leptomeninges. It is estimated to affect 1 in 20,000 to 50,000 live newborns. Patients most frequently have ipsilateral parieto-occipital leptomeningeal angiomatosis and calcifications with cortical atrophy, ipsilateral glaucoma, and a unilateral facial hyperpigmented lesion known as the port-wine stain (PWS). About 40% of SWS patients have an oral vascular abnormality. The buccal mucosa, palate, tongue, floor of the mouth, gingiva, and lips may all exhibit purplish-red staining as a result of intraoral angiomatosis. A 9-year-old boy child with a known diagnosis of SWS reported with a chief complaint of decayed teeth, requiring full mouth rehabilitation. As the patient showed minimal response to verbal commands with apprehension and inability to cooperate on a dental chair, it was decided to do full mouth rehabilitation under general anaesthesia. A thorough understanding of SWS is essential due to the significant frequency of oral symptoms of this uncommon congenital condition. This case report added to the knowledge and understanding of full mouth rehabilitation of a child patient with SWS under GA.