HEMOLYSIS IN A PATIENT WITH WILSON'S DISEASE: A RARE PRESENTATION

Wilson’s disease is an uncommon autosomal recessive inherited disease that is characterized by abnormal copper metabolism with toxic accumulation of copper in a number of organs. Hepatic, neurological, and psychiatric symptoms are frequently observed, whereas hemolytic anemia is an often forgotten sign. We report here the case of a young man with Wilson's disease who presented with acute hemolysis. This case underscores the importance of inclusion of Wilson’s disease in the differential diagnosis of idiopathic hemolytic anemia in young patient and emphasizes the importance of prompt diagnosis and management for a better long-term outcome. Keywords: Wilson disease, Copper deposition disease and Hemolysis