Extrophy of Bladder

Bladder extrophy is an uncommon congenital anomaly of lower abdominal wall which is detected and managed at birth. As the bladder is open there is usually no upper tract involvement in these cases. Upper tract dilatation may be seen after successful bladder neck repair due to associated anatomical vesicoureteric reflux. In this case report we present an unusual association of bladder extrophy with bilateral upper tract involvement prior to bladder neck repair.