Pheochromocytoma and congenital heart diseases : about a case

Abstract Pheochromocytoma is a tumor developed in the deep layer of the adrenal gland from chromaffin cells responsible for hypersecretion of catecholamines. The latter is the cause of vasoactive disorders, namely hypertensive peaks with tachycardia. These induced disorders can be difficult to manage in patients with an underlying cardiac pathology. We report the case of an 18-year-old patient whom we had to treat for left pheochromocytoma. He has been followed since childhood for complex congenital heart disease with left ventricular single heart type. The patient was operated on under general anesthesia with many precautions taken by conventional means without incident. It seemed appropriate to describe this case with a review of the literature for its particularity and rarity