A Case of Congenitally Corrected Transposition of the Great Arteries at Age 75 Years

Congenitally Corrected Transposition of the Great Arteries (CCTGA) is a rare congenital disorder that accounts for less than 1% (~ 0.5%) of all congenital heart malformations.[1] It is described as “double discordance” because both the atrioventricular and ventriculo-arterial connections are inappropriate.[2] CCTGA is usually associated with other abnormalities, including conduction system defects and anatomic anomalies, such as ventricular septal defect (VSD), pulmonary stenosis (PS) and tricuspid valve malformations.[1,2] The clinical presentation depends on the presence or absence of these associated entities[2] The natural history is mainly dictated by the function of the systemic right ventricle and tricuspid valve as well as the existence of concomitant arrhythmias, especially complete heart block.[3] The management of CCTGA remains a serious challenge and depends on the age of the patient, the symptoms and the accompanying defects.[4]