A Tale of Two Atypical Presentations of Desmoplastic Small Round Cell Tumors: A Rare Mesenchymal Tumor

Desmoplastic Small Round Cell Tumor (DSRCT) is a rare malignant mesenchymaltumor that usually arises in the abdomen and pelvis and demonstrates a locallyaggressive behavior with multiple peritoneal implants.The paucity of these cases andvaried clinical presentations leads to a diagnostic dilemma, and there are noconsensusguidelines regarding management. We report 2 unusual presentations of DSRCT, onewith testicular mass along with retroperitoneal lymphnodes and umbilical nodule, andanother with left inguinal swelling and omental mass. These cases are being presentedbecause of infrequent occurrences and unusual presentations that have been notreported in the literature so far