A RARE CASE OF IDIOPATHIC RETROPERITONEAL FIBROSIS
Retroperitoneal Fibrosis (RPF) is a rare fibroinflammatory disorder characterized by the deposition of fibrous tissue in the retroperitoneal space, often involving the abdominal aorta, iliac arteries, and ureters1. Despite its rarity, RPF can lead to significant morbidity, with limited epidemiological data available to guide clinical management. Here, we present the case of an 82-year-old female patient diagnosed with RPF, presenting with gross hematuria as the primary complaint. Our patient's clinical course was complicated by the atypical localization of fibrotic tissue, resulting in diagnostic challenges and necessitating a multidisciplinary approach to management. We discuss the diagnostic workup, including imaging studies, as well as the therapeutic interventions employed, such as corticosteroid therapy and interventional management. This case underscores the importance of considering RPF in the differential diagnosis of patients presenting with renal and urinary tract symptoms, particularly in older adults. By sharing our experience, we aim to contribute to the collective knowledge base and improve the care of future patients with this rare condition.
Publication Details
- Journal
- Zenodo (CERN European Organization for Nuclear Research)
- Published
- 2024-11-10
- DOI
- https://doi.org/10.5281/zenodo.14063745
- Primary Topic
- IgG4-Related and Inflammatory Diseases
- Type
- article
- Field-Weighted Citation Impact
- 0.00