A RARE CASE OF IDIOPATHIC RETROPERITONEAL FIBROSIS

Retroperitoneal Fibrosis (RPF) is a rare fibroinflammatory disorder characterized by the deposition of fibrous tissue in the retroperitoneal space, often involving the abdominal aorta, iliac arteries, and ureters1. Despite its rarity, RPF can lead to significant morbidity, with limited epidemiological data available to guide clinical management. Here, we present the case of an 82-year-old female patient diagnosed with RPF, presenting with gross hematuria as the primary complaint. Our patient's clinical course was complicated by the atypical localization of fibrotic tissue, resulting in diagnostic challenges and necessitating a multidisciplinary approach to management. We discuss the diagnostic workup, including imaging studies, as well as the therapeutic interventions employed, such as corticosteroid therapy and interventional management. This case underscores the importance of considering RPF in the differential diagnosis of patients presenting with renal and urinary tract symptoms, particularly in older adults. By sharing our experience, we aim to contribute to the collective knowledge base and improve the care of future patients with this rare condition.

Publication Details

Journal
Zenodo (CERN European Organization for Nuclear Research)
Published
2024-11-10
DOI
https://doi.org/10.5281/zenodo.14063745
Primary Topic
IgG4-Related and Inflammatory Diseases
Type
article
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article

A RARE CASE OF IDIOPATHIC RETROPERITONEAL FIBROSIS

Zenodo (CERN European Organization for Nuclear Research)
IgG4-Related and Inflammatory Diseases
article

A RARE CASE OF IDIOPATHIC RETROPERITONEAL FIBROSIS

article en

Abstract

Retroperitoneal Fibrosis (RPF) is a rare fibroinflammatory disorder characterized by the deposition of fibrous tissue in the retroperitoneal space, often involving the abdominal aorta, iliac arteries, and ureters1. Despite its rarity, RPF can lead to significant morbidity, with limited epidemiological data available to guide clinical management. Here, we present the case of an 82-year-old female patient diagnosed with RPF, presenting with gross hematuria as the primary complaint. Our patient's clinical course was complicated by the atypical localization of fibrotic tissue, resulting in diagnostic challenges and necessitating a multidisciplinary approach to management. We discuss the diagnostic workup, including imaging studies, as well as the therapeutic interventions employed, such as corticosteroid therapy and interventional management. This case underscores the importance of considering RPF in the differential diagnosis of patients presenting with renal and urinary tract symptoms, particularly in older adults. By sharing our experience, we aim to contribute to the collective knowledge base and improve the care of future patients with this rare condition.

Zenodo (CERN European Organization for Nuclear Research)
Good health and well-being
Openalex Percentile: Top 53%
IgG4-Related and Inflammatory Diseases
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