A Review of Amniotic Band Syndrome

Amniotic Band Syndrome (ABS) is a rare congenital anomaly characterized by fibrous bands that entangle and constrict fetal limbs, causing various deformities and complications. ABS occurs due to amniotic sac damage, leading to fibrous band formation. Clinical features include limb deformities, craniofacial abnormalities, and gastrointestinal and genitourinary tract defects. Diagnosis is primarily prenatal via ultrasound. Management involves multidisciplinary care, including prenatal surgery, postnatal surgical reconstruction, and long-term rehabilitation.

Publication Details

Journal
Zenodo (CERN European Organization for Nuclear Research)
Published
2024-10-07
DOI
https://doi.org/10.5281/zenodo.13897822
Primary Topic
Congenital Anomalies and Fetal Surgery
Type
article
Field-Weighted Citation Impact
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article

A Review of Amniotic Band Syndrome

Zenodo (CERN European Organization for Nuclear Research)
Congenital Anomalies and Fetal Surgery
article

A Review of Amniotic Band Syndrome

article en

Abstract

Amniotic Band Syndrome (ABS) is a rare congenital anomaly characterized by fibrous bands that entangle and constrict fetal limbs, causing various deformities and complications. ABS occurs due to amniotic sac damage, leading to fibrous band formation. Clinical features include limb deformities, craniofacial abnormalities, and gastrointestinal and genitourinary tract defects. Diagnosis is primarily prenatal via ultrasound. Management involves multidisciplinary care, including prenatal surgery, postnatal surgical reconstruction, and long-term rehabilitation.

Zenodo (CERN European Organization for Nuclear Research)
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Openalex Percentile: Top 50%
Congenital Anomalies and Fetal Surgery
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A Review of Amniotic Band Syndrome · Zenodo (CERN European Organization for Nuclear Research) (2024) | TGRS Research Map | TGRS