Catecholaminergic polymorphic ventricular tachycardia mediated by ryanodine receptor 2: a validated risk stratification

These externally validated risk prediction models using clinical parameters accurately distinguished CPVT patients on β-blocker monotherapy at low and high risk for future AEs while treated with β-blockers. These models provide guidance for implementation of clinical management therapies to prevent AEs in patients with CPVT.

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Publication Details

Journal
European Heart Journal
Published
2025-11-09
DOI
https://doi.org/10.1093/eurheartj/ehaf965
Citations
1
Primary Topic
Cardiac electrophysiology and arrhythmias
Type
article
Field-Weighted Citation Impact
1.39
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article

Catecholaminergic polymorphic ventricular tachycardia mediated by ryanodine receptor 2: a validated risk stratification

1 citations
European Heart Journal
Cardiac electrophysiology and arrhythmias
1.39
article

Catecholaminergic polymorphic ventricular tachycardia mediated by ryanodine receptor 2: a validated risk stratification

article en
1 citations

Abstract

These externally validated risk prediction models using clinical parameters accurately distinguished CPVT patients on β-blocker monotherapy at low and high risk for future AEs while treated with β-blockers. These models provide guidance for implementation of clinical management therapies to prevent AEs in patients with CPVT.

European Heart Journal
Universidad de Las Palmas de Gran Canaria (ES), University of Copenhagen (DK), Western University (CA), Oslo University Hospital (NO), Heart Rhythm Society (US), Centre National de la Recherche Scientifique (FR), The University of Sydney (AU), Hospital Sant Joan de Déu Barcelona (ES), Royal Children's Hospital (AU), Mayo Clinic (US), University Medical Center Groningen (NL), University of Helsinki (FI), Garvan Institute of Medical Research (AU), University of British Columbia (CA), Université de Bordeaux (FR), University of Auckland (NZ), Inserm (FR), Shiga University of Medical Science (JP), Universitat de València (ES), The University of Melbourne (AU), City, University of London (GB), Université Paris Cité (FR), Charles University (CZ), Heidelberg University (DE), Universitat de Girona (ES), Royal Prince Alfred Hospital (AU), Tel Aviv Sourasky Medical Center (IL), Leiden University Medical Center (NL), Great Ormond Street Hospital (GB), Helsinki University Hospital (FI), Centenary Institute (AU), London Health Sciences Centre (CA), St George’s University Hospitals NHS Foundation Trust (GB), Instituto de Salud Carlos III (ES), Erasmus MC (NL), University Hospital Heidelberg (DE), Rigshospitalet (DK), Population Health Research Institute (CA), Hospital Universitari i Politècnic La Fe (ES), Electrophysiology and Heart Modeling Institute (FR), Azienda Ospedaliera Citta' della Salute e della Scienza di Torino (IT), Centro de Investigación en Red en Enfermedades Cardiovasculares (ES), Emma Kinderziekenhuis (NL), Royal Brompton Hospital (GB), University Hospital in Motol (CZ), Bordeaux Population Health (FR), Amsterdam Neuroscience (NL), National Cerebral and Cardiovascular Center (JP), Institut d'Investigació Biomèdica de Girona (ES), Centro de Investigación Biomédica en Red (ES), Bambino Gesù Children's Hospital (IT), Mayo Clinic in Arizona (US), Department of Medical Sciences (BY), Willem-Alexander Kinderziekenhuis (NL), Saitama International Medical Center (JP), IRCCS Istituto Auxologico Italiano (IT), Erasmus MC - Sophia Children’s Hospital (NL), ERN GUARD-Heart (NL), Institut du Thorax (FR), Starship Children's Health (NZ), Hôpital Bichat-Claude-Bernard (FR), Mayo Clinic in Florida (US), Hospital General de Elda (ES), Servicio Murciano de Salud (ES), Murdoch Children's Research Institute (AU), Amsterdam University Medical Centers (NL), BC Children's Hospital (CA), Hospital Universitari de Girona Doctor Josep Trueta (ES), University Medical Centre Mannheim (DE), Smith Clinic (US), Instituto de Investigación Sanitaria La Fe (ES), University College London (GB), Amsterdam University of Applied Sciences (NL), University of Milano-Bicocca (IT), Universidad de Murcia (ES), Nippon Medical School (JP), Saitama Medical University (JP), University of Amsterdam (NL), Vanderbilt University Medical Center (US), Umeå University (SE), KU Leuven (BE)
Openalex Percentile: Top 13%
Cardiac electrophysiology and arrhythmias
1.39
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