Outcomes of Patients With Arrhythmia During Single‐Ventricle Palliation

This study evaluates the outcomes of patients with single-ventricle physiology and arrhythmias occurring before Fontan surgery, examining the relationship between early arrhythmias and clinical outcomes. Conducted as a single-center retrospective analysis from August 2011 to January 2024, it includes 109 patients with hypoplastic left heart syndrome. Arrhythmias were common during Stage 1 admission (97%). Pre-Fontan electrophysiology studies showed inducible tachycardia in 33% of patients, with ablation needed in those with heterotaxy syndrome and complex tachycardia. Survival to Fontan was poor, with significant mortality at each stage. Tailored arrhythmia monitoring and management strategies are essential.