Prognostic role of myocardial storage, hypertrophy, and inflammation/fibrosis in Fabry cardiomyopathy: a new predictive score including T1 values

We propose a 3-years prognostic score to predict CV outcome in FD, including age, LVMI, number of LGE+ segments, and septal T1. Normal T1 has a negative predictive value for adverse CV events irrespective of the acquisition setting.

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Publication Details

Journal
European Heart Journal - Quality of Care and Clinical Outcomes
Published
2025-12-12
DOI
https://doi.org/10.1093/ehjqcco/qcaf154
Citations
2
Primary Topic
Lysosomal Storage Disorders Research
Type
article
Field-Weighted Citation Impact
2.33
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article

Prognostic role of myocardial storage, hypertrophy, and inflammation/fibrosis in Fabry cardiomyopathy: a new predictive score including T1 values

Marta Ferraresi, Lara Tondi, Pietro Spagnolo, Laura Econimo et al.
2 citations
European Heart Journal - Quality of Care and Clinical Outcomes
Lysosomal Storage Disorders Research
2.33
article

Prognostic role of myocardial storage, hypertrophy, and inflammation/fibrosis in Fabry cardiomyopathy: a new predictive score including T1 values

Marta Ferraresi, Lara Tondi, Pietro Spagnolo, Laura Econimo, Andrea F. Attanasio, Paola Lusardi, Giandomenico Disabato, Kelvin Chow, Antonia Camporeale, Alessandro P. Burlina, Maurizio Pieroni, Valentina Milani, Massimo Lombardi, Federico Pieruzzi, Federico Ambrogi, Gianpaolo Carrafiello, Renzo Mignani, Giada De Angeli, Gianluigi Guida
article en
2 citations

Abstract

We propose a 3-years prognostic score to predict CV outcome in FD, including age, LVMI, number of LGE+ segments, and septal T1. Normal T1 has a negative predictive value for adverse CV events irrespective of the acquisition setting.

European Heart Journal - Quality of Care and Clinical Outcomes
University of Milan (IT), Agostino Gemelli University Polyclinic (IT), Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico (IT), IRCCS Policlinico San Donato (IT), Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia (IT), Ospedale Humanitas Gradenigo (IT), Azienda Ospedaliera San Gerardo (IT), Azienda Ospedaliero-Universitaria Careggi (IT), Medical Solutions (GB), Ospedale San Bassiano (IT), Ospedale Infermi di Rimini (IT), Siemens Healthcare (United States) (US), University of Florence (IT), University of Milano-Bicocca (IT)
Openalex Percentile: Top 10%
Lysosomal Storage Disorders Research
2.33
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