Prognostic role of myocardial storage, hypertrophy, and inflammation/fibrosis in Fabry cardiomyopathy: a new predictive score including T1 values
We propose a 3-years prognostic score to predict CV outcome in FD, including age, LVMI, number of LGE+ segments, and septal T1. Normal T1 has a negative predictive value for adverse CV events irrespective of the acquisition setting.
Authors
- Marta Ferraresi
- Lara Tondi (ORCID: https://orcid.org/0000-0001-7140-0341)
- Pietro Spagnolo (ORCID: https://orcid.org/0000-0003-0914-314X)
- Laura Econimo
- Andrea F. Attanasio (ORCID: https://orcid.org/0000-0002-8007-2324)
- Paola Lusardi
- Giandomenico Disabato (ORCID: https://orcid.org/0000-0003-1024-1644)
- Kelvin Chow (ORCID: https://orcid.org/0000-0003-0698-1746)
- Antonia Camporeale (ORCID: https://orcid.org/0000-0001-7604-0496)
- Alessandro P. Burlina (ORCID: https://orcid.org/0000-0002-2224-4706)
- Maurizio Pieroni (ORCID: https://orcid.org/0000-0002-6830-4292)
- Valentina Milani (ORCID: https://orcid.org/0000-0002-2989-981X)
- Massimo Lombardi (ORCID: https://orcid.org/0000-0003-1700-8749)
- Federico Pieruzzi (ORCID: https://orcid.org/0000-0002-1302-6846)
- Federico Ambrogi (ORCID: https://orcid.org/0000-0001-9358-011X)
- Gianpaolo Carrafiello (ORCID: https://orcid.org/0000-0002-8002-4277)
- Renzo Mignani (ORCID: https://orcid.org/0000-0001-8507-8939)
- Giada De Angeli (ORCID: https://orcid.org/0000-0003-2826-0181)
- Gianluigi Guida (ORCID: https://orcid.org/0009-0003-5666-8368)
Institutions
- University of Milan (IT)
- Agostino Gemelli University Polyclinic (IT)
- Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico (IT)
- IRCCS Policlinico San Donato (IT)
- Azienda Socio Sanitaria Territoriale degli Spedali Civili di Brescia (IT)
- Ospedale Humanitas Gradenigo (IT)
- Azienda Ospedaliera San Gerardo (IT)
- Azienda Ospedaliero-Universitaria Careggi (IT)
- Medical Solutions (GB)
- Ospedale San Bassiano (IT)
- Ospedale Infermi di Rimini (IT)
- Siemens Healthcare (United States) (US)
- University of Florence (IT)
- University of Milano-Bicocca (IT)
Publication Details
- Journal
- European Heart Journal - Quality of Care and Clinical Outcomes
- Published
- 2025-12-12
- DOI
- https://doi.org/10.1093/ehjqcco/qcaf154
- Citations
- 2
- Primary Topic
- Lysosomal Storage Disorders Research
- Type
- article
- Field-Weighted Citation Impact
- 2.33