Prognostic factors and a nomogram for survival in anti-MDA5 antibody-positive dermatomyositis-associated interstitial lung disease

Anti-MDA5 antibody positivity was strongly associated with higher short-term mortality in DM-ILD. The proposed nomogram, integrating RP-ILD, ALB, CRP, ferritin, and NLR, showed robust predictive accuracy and may aid individualized risk stratification. External validation is warranted.

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Publication Details

Journal
BMC Pulmonary Medicine
Published
2025-12-09
DOI
https://doi.org/10.1186/s12890-025-04031-y
Primary Topic
Inflammatory Myopathies and Dermatomyositis
Type
article
Field-Weighted Citation Impact
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article

Prognostic factors and a nomogram for survival in anti-MDA5 antibody-positive dermatomyositis-associated interstitial lung disease

Zhaohui Tong, Baolu Yang
BMC Pulmonary Medicine
Inflammatory Myopathies and Dermatomyositis
article

Prognostic factors and a nomogram for survival in anti-MDA5 antibody-positive dermatomyositis-associated interstitial lung disease

Zhaohui Tong, Baolu Yang
article en

Abstract

Anti-MDA5 antibody positivity was strongly associated with higher short-term mortality in DM-ILD. The proposed nomogram, integrating RP-ILD, ALB, CRP, ferritin, and NLR, showed robust predictive accuracy and may aid individualized risk stratification. External validation is warranted.

BMC Pulmonary MedicineVol. 25(1)
Beijing Tongren Hospital (CN), Capital Medical University (CN), Beijing Chao-Yang Hospital, Capital Medical University (CN)
Openalex Percentile: Top 49%
Inflammatory Myopathies and Dermatomyositis
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