Paediatric pulmonary arterial hypertension following congenital heart defect repair: enhanced risk stratification and outcomes in a national cohort
In this national cohort of children with repaired PAH-CHD, mortality is significant. This novel, simple risk score has been developed and validated specifically for children with repaired PAH-CHD, useful at the time of post-operative assessment to predict outcome and direct management.
Authors
- Konstantinos Dimopoulos (ORCID: https://orcid.org/0000-0003-1300-0504)
- M Ángeles Izquierdo Riezu
- Alejandro Rodríguez Ogando (ORCID: https://orcid.org/0000-0003-4424-9409)
- Francesca Perín (ORCID: https://orcid.org/0000-0003-1041-930X)
- Katrijn Jansen (ORCID: https://orcid.org/0000-0002-6576-359X)
- Helen Michael (ORCID: https://orcid.org/0000-0002-8326-0806)
- Shahin Moledina (ORCID: https://orcid.org/0000-0003-0262-2340)
- Joydeep Mookerjee
- Kaushiga Krishnathasan (ORCID: https://orcid.org/0000-0002-7097-6012)
- Antonio Moreno (ORCID: https://orcid.org/0000-0002-2496-9786)
- W. Brodie Knight
- SJ Wort
- Paul Clift (ORCID: https://orcid.org/0000-0001-8906-7647)
- Grace Chaplin (ORCID: https://orcid.org/0000-0001-7901-1850)
- Amparo Moya Bonora
- Andrew Constantine (ORCID: https://orcid.org/0000-0001-7899-463X)
- Robin Condliffe (ORCID: https://orcid.org/0000-0002-3492-4143)
- Alberto Mendoza Soto
- Inmaculada Guillén Rodríguez
- Caroline B. Jones (ORCID: https://orcid.org/0000-0002-5105-6384)
- María J Del Cerro Marín
- Marta López Ramón
- Carlos Labrandero de Lera (ORCID: https://orcid.org/0009-0006-4806-1891)
- Juana M Espín López
- Rami Dhillon
- Sandra Villagrá Albert
- Maria Nieves Velasco Forte
- Dirk G. Wilson
Institutions
- Leeds General Infirmary (GB)
- University Hospitals Birmingham NHS Foundation Trust (GB)
- Leeds Teaching Hospitals NHS Trust (GB)
- Royal Brompton & Harefield NHS Foundation Trust (GB)
- NHS Greater Glasgow and Clyde (GB)
- Great Ormond Street Hospital for Children NHS Foundation Trust (GB)
- Royal Hospital for Children (GB)
- Hospital Universitario La Paz (ES)
- University Hospitals Bristol NHS Foundation Trust (GB)
- University Hospital of Wales (GB)
- Newcastle upon Tyne Hospitals NHS Foundation Trust (GB)
- Royal Hallamshire Hospital (GB)
- Bristol Royal Hospital for Children (GB)
- Hospital General Universitario Gregorio Marañón (ES)
- Hospital Universitari i Politècnic La Fe (ES)
- University of Alabama at Birmingham (US)
- Research Institute Hospital 12 de Octubre (ES)
- Alder Hey Children's NHS Foundation Trust (GB)
- Royal Brompton Hospital (GB)
- Department of Science and Technology (IN)
- Biogipuzkoa Health Research Institute (ES)
- Lung Institute (US)
- Hospital Universitario Miguel Servet (ES)
- Hospital Universitario Virgen de las Nieves (ES)
- Unidades Centrales Científico-Técnicas (ES)
- Clínica Santa María (CO)
- Vall d'Hebron Hospital Universitari (ES)
- Donostiako Unibertsitate Ospitalea (ES)
- Hospital Universitario Virgen de la Arrixaca (ES)
- Hospital Universitario Virgen del Rocío (ES)
- Hospital de Clínicas (UY)
- Birmingham Women’s and Children’s NHS Foundation Trust (GB)
- Royal Manchester Children's Hospital (GB)
- Hospital Universitario Ramón y Cajal (ES)
- University College London (GB)
- Imperial College London (GB)
- University of Birmingham (GB)
- Newcastle University (GB)
Publication Details
- Journal
- European Heart Journal - Quality of Care and Clinical Outcomes
- Published
- 2025-12-05
- DOI
- https://doi.org/10.1093/ehjqcco/qcaf150
- Citations
- 1
- Primary Topic
- Pulmonary Hypertension Research and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 1.52