Nonsystemic Vasculitic Neuropathy—A Brazilian Case Series

These findings highlight that NSVN often presents with painful sensorimotor symptoms and may clinically mimic progressive axonal polyneuropathies. Given its potential for significant morbidity if left untreated, early recognition and consideration of nerve biopsy remain critical. The diagnostic complexity and variability in presentation suggest that NSVN may be underrecognized. We hope this cohort contributes to a broader understanding of its clinical spectrum and informs future diagnostic strategies.

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Publication Details

Journal
Journal of the Peripheral Nervous System
Published
2025-12-01
DOI
https://doi.org/10.1111/jns.70086
Primary Topic
Vasculitis and related conditions
Type
article
Field-Weighted Citation Impact
0.00
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article

Nonsystemic Vasculitic Neuropathy—A Brazilian Case Series

Salim Lázaro Balassiano, Manuella Lima Gomes Ochtrop, Márcia Rodrigues Jardim, Roberto Pereira Santos et al.
Journal of the Peripheral Nervous System
Vasculitis and related conditions
article

Nonsystemic Vasculitic Neuropathy—A Brazilian Case Series

Salim Lázaro Balassiano, Manuella Lima Gomes Ochtrop, Márcia Rodrigues Jardim, Roberto Pereira Santos, Victor Evangelista Rodrigues Pereira, Marcos RG de Freitas, Ana Caroline Siquara‐De‐Souza
article en

Abstract

These findings highlight that NSVN often presents with painful sensorimotor symptoms and may clinically mimic progressive axonal polyneuropathies. Given its potential for significant morbidity if left untreated, early recognition and consideration of nerve biopsy remain critical. The diagnostic complexity and variability in presentation suggest that NSVN may be underrecognized. We hope this cohort contributes to a broader understanding of its clinical spectrum and informs future diagnostic strategies.

Journal of the Peripheral Nervous SystemVol. 30(4)
Universidade Federal do Rio de Janeiro (BR), Hospital Universitário Pedro Ernesto (BR), Hospital Universitário Clementino Fraga Filho (BR), Fundação Oswaldo Cruz (BR)
Openalex Percentile: Top 42%
Vasculitis and related conditions
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Nonsystemic Vasculitic Neuropathy—A Brazilian Case Series — Salim Lázaro Balassiano, Manuella Lima Gomes Ochtrop, et al. · Journal of the Peripheral Nervous System (2025) | TGRS Research Map | TGRS