Nonsystemic Vasculitic Neuropathy—A Brazilian Case Series
These findings highlight that NSVN often presents with painful sensorimotor symptoms and may clinically mimic progressive axonal polyneuropathies. Given its potential for significant morbidity if left untreated, early recognition and consideration of nerve biopsy remain critical. The diagnostic complexity and variability in presentation suggest that NSVN may be underrecognized. We hope this cohort contributes to a broader understanding of its clinical spectrum and informs future diagnostic strategies.
Authors
- Salim Lázaro Balassiano
- Manuella Lima Gomes Ochtrop
- Márcia Rodrigues Jardim (ORCID: https://orcid.org/0000-0003-1784-6857)
- Roberto Pereira Santos (ORCID: https://orcid.org/0000-0002-9862-6057)
- Victor Evangelista Rodrigues Pereira (ORCID: https://orcid.org/0000-0001-7147-6418)
- Marcos RG de Freitas (ORCID: https://orcid.org/0000-0001-7747-0287)
- Ana Caroline Siquara‐De‐Souza
Institutions
- Universidade Federal do Rio de Janeiro (BR)
- Hospital Universitário Pedro Ernesto (BR)
- Hospital Universitário Clementino Fraga Filho (BR)
- Fundação Oswaldo Cruz (BR)
Publication Details
- Journal
- Journal of the Peripheral Nervous System
- Published
- 2025-12-01
- DOI
- https://doi.org/10.1111/jns.70086
- Primary Topic
- Vasculitis and related conditions
- Type
- article
- Field-Weighted Citation Impact
- 0.00