Moya Moya Disease in Pregnancy – Dilemmas in Management

Abstract Moya Moya disease (MMD) represents an unusual cerebrovascular pathology where an initial phase of obliterative vasculopathy of the large intracranial vessels is replaced by a compensatory phase of proliferative vasculopathy of the small perforators. Pregnancy in patients with MMD carries a high risk of cerebrovascular events which can adversely affect both the mother and fetus. We share our experience with a hemorrhagic MMD in a pregnant middle-aged woman and discuss the management dilemmas.