Cardiac characteristics of Fabry disease from baseline enrolment data in a nationwide prospective Japanese registry

As the first large-scale prospective registry of FD patients in Japan, this study has provided valuable baseline data for the cardiac features and management of FD.

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Publication Details

Journal
International Journal of Cardiology
Published
2025-12-04
DOI
https://doi.org/10.1016/j.ijcard.2025.134071
Primary Topic
Lysosomal Storage Disorders Research
Type
article
Field-Weighted Citation Impact
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article

Cardiac characteristics of Fabry disease from baseline enrolment data in a nationwide prospective Japanese registry

Yuki Kuramoto, Hiroki Ikenaga, Yoshiharu Kinugasa, Kenichi Tsujita et al.
International Journal of Cardiology
Lysosomal Storage Disorders Research
article

Cardiac characteristics of Fabry disease from baseline enrolment data in a nationwide prospective Japanese registry

Yuki Kuramoto, Hiroki Ikenaga, Yoshiharu Kinugasa, Kenichi Tsujita, Yuya Matsue, Hiromitsu Kanamori, Hiroaki Kitaoka, Takahiro Kanda, Kenji Onoue, Yuichiro Iida, Toru Kubo, Toshiyuki Yano, K. Nakamura, Yuji Nagatomo, Naoki Nakagawa, Keisuke Kida, Hiroyuki Yamakawa, Masashi Amano, Yuichiro Maekawa, Saori Yamamoto, Koji Higuchi, Atsushi Suzuki, Yu Yamada, Yasuhiro Izumiya, Toshiyuki Nagai, Masayoshi Oikawa, Hiroshi Ito, Kazufumi Nakamura, Hideo Izawa, Kenichi Hongo
article en

Abstract

As the first large-scale prospective registry of FD patients in Japan, this study has provided valuable baseline data for the cardiac features and management of FD.

International Journal of CardiologyVol. 445
Kagoshima University (JP), Hiroshima University (JP), Jikei University School of Medicine (JP), Fukushima Medical University (JP), Sapporo Medical University (JP), Fujita Health University (JP), University of Tsukuba (JP), Asahikawa Medical University (JP), St. Marianna University School of Medicine (JP), Tohoku University (JP), Keio University (JP), Hokkaido University (JP), Hamamatsu University School of Medicine (JP), Juntendo University (JP), Takamatsu Red Cross Hospital (JP), Okayama University Hospital (JP), National Cerebral and Cardiovascular Center (JP), Mie University Hospital (JP), Tokyo Women's Medical University (JP), Gifu University (JP), Tottori University (JP), National Defense Medical College (JP), Kitasato University (JP), Nara Medical University (JP), University of Yamanashi (JP), Kōchi University (JP), Kumamoto University (JP)
Openalex Percentile: Top 52%
Lysosomal Storage Disorders Research
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