New Validated Staging System for Light Chain (AL) Amyloidosis With Stage IIIC Defining Ultra-Poor Risk: AL International Staging System

This defines and validates a new staging system from systemic AL amyloidosis with robust identification of an ultra-poor risk stage (IIIC) in contemporarily treated patients.

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Publication Details

Journal
Journal of Clinical Oncology
Published
2025-12-07
DOI
https://doi.org/10.1200/jco-25-02558
Primary Topic
Amyloidosis: Diagnosis, Treatment, Outcomes
Type
article
Field-Weighted Citation Impact
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article

New Validated Staging System for Light Chain (AL) Amyloidosis With Stage IIIC Defining Ultra-Poor Risk: AL International Staging System

Angela A. Dispenzieri, Morie A. Gertz, Valeria Di Simone, Efstathios Kastritis et al.
Journal of Clinical Oncology
Amyloidosis: Diagnosis, Treatment, Outcomes
article

New Validated Staging System for Light Chain (AL) Amyloidosis With Stage IIIC Defining Ultra-Poor Risk: AL International Staging System

Angela A. Dispenzieri, Morie A. Gertz, Valeria Di Simone, Efstathios Kastritis, Amy A. Kirkwood, Helen Jane Lachmann, Roberta Mussinelli, Shaji Kunnathu Kumar, Lucia Venneri, Oliver Charles Cohen, Monique C. Minnema, Marianna Fontana, Αlexandros Briasoulis, Julian D. Gillmore, Carol Jane Whelan, Jahanzaib Khwaja, Foteini Theodorakakou, Sriram Ravichandran, Ashutosh D. Wechalekar, Κimon Stamatelopoulos, Eli Muchtar, Marish I.F.J. Oerlemans, Giovanni O. Palladini, Paolo Milani, Rahel Schwotzer, Binoy Yohannan, Flores Weverling, Ιoannis Petropoulos, Shameem Mahmood
article en

Abstract

This defines and validates a new staging system from systemic AL amyloidosis with robust identification of an ultra-poor risk stage (IIIC) in contemporarily treated patients.

Journal of Clinical OncologyVol. 44(4)
Utrecht University (NL), National and Kapodistrian University of Athens (GR), University of Pavia (IT), Royal London Hospital (GB), University Medical Center Utrecht (NL), University Hospital of Zurich (CH), Amyloidosis Foundation (US), Alexandra Hospital (GR), Mayo Clinic in Arizona (US), CRUK Lung Cancer Centre of Excellence (GB), Policlinico San Matteo Fondazione (IT), Istituti di Ricovero e Cura a Carattere Scientifico (IT), University College London (GB)
Openalex Percentile: Top 65%
Amyloidosis: Diagnosis, Treatment, Outcomes
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