Classification of interstitial pneumonias: ready for the future or stuck in the past?

<title>Extract</title> Interstitial lung diseases (ILDs) or interstitial pneumonias (IPs) are a large group of rare diffuse lung diseases that primarily affect the interstitial space, alveoli and, to a lesser extent, the small airways and pulmonary vasculature. The classification and grouping of diseases in “boxes” has been an important element of medicine for decades, if not centuries. Disease classification aims at better describing disease entities, providing details for making a proper diagnosis and developing the rationale for disease-specific management. Good classifications, therefore, serve both clinical care and clinical research.

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Publication Details

Journal
European Respiratory Journal
Published
2025-12-01
DOI
https://doi.org/10.1183/13993003.01845-2025
Primary Topic
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
Type
article
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article

Classification of interstitial pneumonias: ready for the future or stuck in the past?

Vincent Cottin, Bruno Crestani, Martin Kolb
European Respiratory Journal
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
article

Classification of interstitial pneumonias: ready for the future or stuck in the past?

Vincent Cottin, Bruno Crestani, Martin Kolb
article en

Abstract

<title>Extract</title> Interstitial lung diseases (ILDs) or interstitial pneumonias (IPs) are a large group of rare diffuse lung diseases that primarily affect the interstitial space, alveoli and, to a lesser extent, the small airways and pulmonary vasculature. The classification and grouping of diseases in “boxes” has been an important element of medicine for decades, if not centuries. Disease classification aims at better describing disease entities, providing details for making a proper diagnosis and developing the rationale for disease-specific management. Good classifications, therefore, serve both clinical care and clinical research.

European Respiratory JournalVol. 66(6)
Inserm (FR), Université Paris Cité (FR), Institut National de Recherche pour l'Agriculture, l'Alimentation et l'Environnement (FR), Assistance Publique – Hôpitaux de Paris (FR), Centre de Recherche sur l'Inflammation (FR), Hôpital Louis Pradel (FR), Hôpital Bichat-Claude-Bernard (FR), St. Joseph’s Healthcare Hamilton (CA)
Openalex Percentile: Top 43%
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
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Classification of interstitial pneumonias: ready for the future or stuck in the past? — Vincent Cottin, Bruno Crestani, et al. · European Respiratory Journal (2025) | TGRS Research Map | TGRS