<scp>VEXAS</scp> Syndrome Presenting With Pleuritis

Elderly men with pleuritis, systemic inflammation, cytopenias, and bone-marrow vacuolization may have VEXAS due to somatic <i>UBA1</i> mutations. Pulmonary involvement, including pleuritis, can be a key presentation despite the absence of classic chondritis, and early recognition may enable timely initiation of corticosteroid therapy.

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Publication Details

Journal
Clinical Case Reports
Published
2025-12-01
DOI
https://doi.org/10.1002/ccr3.71590
Primary Topic
Otitis Media and Relapsing Polychondritis
Type
article
Field-Weighted Citation Impact
0.00
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article

VEXAS Syndrome Presenting With Pleuritis

Takahiko Yasuda, Norio Takagi, Makoto Ito, Yasushi Murakami et al.
Clinical Case Reports
Otitis Media and Relapsing Polychondritis
article

VEXAS Syndrome Presenting With Pleuritis

Takahiko Yasuda, Norio Takagi, Makoto Ito, Yasushi Murakami, Michita Suzuki
article en

Abstract

Elderly men with pleuritis, systemic inflammation, cytopenias, and bone-marrow vacuolization may have VEXAS due to somatic <i>UBA1</i> mutations. Pulmonary involvement, including pleuritis, can be a key presentation despite the absence of classic chondritis, and early recognition may enable timely initiation of corticosteroid therapy.

Clinical Case ReportsVol. 13(12)
National Hospital Organization (JP), Nagoya Medical Center (JP), Tokushima Municipal Hospital (JP), Nagoya University (JP)
Openalex Percentile: Top 46%
Otitis Media and Relapsing Polychondritis
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