<scp>VEXAS</scp> Syndrome Presenting With Pleuritis
Elderly men with pleuritis, systemic inflammation, cytopenias, and bone-marrow vacuolization may have VEXAS due to somatic <i>UBA1</i> mutations. Pulmonary involvement, including pleuritis, can be a key presentation despite the absence of classic chondritis, and early recognition may enable timely initiation of corticosteroid therapy.
Authors
- Takahiko Yasuda (ORCID: https://orcid.org/0000-0002-4686-0976)
- Norio Takagi (ORCID: https://orcid.org/0000-0001-5801-1050)
- Makoto Ito (ORCID: https://orcid.org/0000-0003-4252-2061)
- Yasushi Murakami
- Michita Suzuki
Institutions
- National Hospital Organization (JP)
- Nagoya Medical Center (JP)
- Tokushima Municipal Hospital (JP)
- Nagoya University (JP)
Publication Details
- Journal
- Clinical Case Reports
- Published
- 2025-12-01
- DOI
- https://doi.org/10.1002/ccr3.71590
- Primary Topic
- Otitis Media and Relapsing Polychondritis
- Type
- article
- Field-Weighted Citation Impact
- 0.00