Clinical presentation, treatment, and outcome of children with primary intestinal lymphangiectasia: A national retrospective study
Most children with PIL responded to diet therapy and about a quarter of the cohort had a good prognosis with complete remission even after discontinuation of the diet. Presence of lymphedema or a genetic variant was associated with a chronic condition.
Authors
- H. Clouzeau
- S. Willot
- A. Dabadie
- A. Sabard
- Emmanuelle Ecochard‐Dugelay (ORCID: https://orcid.org/0000-0003-3964-3073)
- Béatrice Dubern (ORCID: https://orcid.org/0000-0002-0065-5344)
- Cécile Lambe (ORCID: https://orcid.org/0000-0002-0265-8725)
- Aurélie Comte (ORCID: https://orcid.org/0000-0003-4073-2524)
- Pierre Poinsot (ORCID: https://orcid.org/0000-0002-5992-8335)
- E. Chaillou
- Julie Rebeuh
- Alexandre Fabre
- Noémie Goret (ORCID: https://orcid.org/0009-0004-1223-5314)
Institutions
- Hôpital Necker-Enfants Malades (FR)
- Université Paris Cité (FR)
- Sorbonne Université (FR)
- Hôpital Femme Mère Enfant (FR)
- Hôpital Armand-Trousseau (FR)
- Centre Hospitalier Universitaire de Besançon (FR)
- Centre Hospitalier Universitaire de Tours (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- Hôpital Pellegrin (FR)
- Centre Hospitalier Universitaire d'Angers (FR)
- Hôpital Robert-Debré (FR)
- Hôpitaux Universitaires de Strasbourg (FR)
- Hôpital des Enfants (FR)
- Centre Hospitalier Universitaire de Rennes (FR)
- Hôpital de la Timone (FR)
Publication Details
- Journal
- Journal of Pediatric Gastroenterology and Nutrition
- Published
- 2025-11-23
- DOI
- https://doi.org/10.1002/jpn3.70266
- Primary Topic
- Lymphatic Disorders and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00