A Rare Presentation of HLH as acute encephalopathy, fever and Diabetic Ketoacidosis (DKA) followed by massive pulmonary embolism: Diagnostic and Therapeutic Challenges.

This case underscores the diagnostic challenge of HLH presenting as metabolic crisis and highlights the importance of early consideration of HLH in patients with unexplained inflammatory and hematologic derangements. Clinicians should also remain vigilant for thromboembolic complications during HLH treatment.