Fontan-Associated Liver Disease

Abstract Fontan-associated liver disease (FALD) is a ubiquitous complication in patients with Fontan physiology. Optimal monitoring of FALD development typically starts with imaging. Liver stiffness values can help guide therapy and can act as a surrogate for disease severity. When nodules are present, they can be challenging. Looking for a lesion that behaves differently than other lesions is the best way to identify hepatocellular carcinoma.