The MAGIC (Mouth and Genital Ulcers With Inflamed Cartilage) of VEXAS: A Case of Overlap Between Behçet Disease and VEXAS Syndrome

Behçet disease (BD) is a chronic multisystem inflammatory condition affecting young to middle-aged adults, typically presenting with oral and genital ulcers, uveitis, and various systemic manifestations. The 1990 International Study Group criteria required recurrent oral ulcers for BD diagnosis, whereas the 2014 International Criteria for BD improved sensitivity through a point-based system.<sup>1</sup>

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Publication Details

Journal
The Journal of Rheumatology
Published
2025-11-15
DOI
https://doi.org/10.3899/jrheum.2025-0924
Primary Topic
Otitis Media and Relapsing Polychondritis
Type
article
Field-Weighted Citation Impact
0.00
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article

The MAGIC (Mouth and Genital Ulcers With Inflamed Cartilage) of VEXAS: A Case of Overlap Between Behçet Disease and VEXAS Syndrome

Amir Bieber, Elia Touma, Shay Brikman, Nadeem Shorbaji
The Journal of Rheumatology
Otitis Media and Relapsing Polychondritis
article

The MAGIC (Mouth and Genital Ulcers With Inflamed Cartilage) of VEXAS: A Case of Overlap Between Behçet Disease and VEXAS Syndrome

Amir Bieber, Elia Touma, Shay Brikman, Nadeem Shorbaji
article en

Abstract

Behçet disease (BD) is a chronic multisystem inflammatory condition affecting young to middle-aged adults, typically presenting with oral and genital ulcers, uveitis, and various systemic manifestations. The 1990 International Study Group criteria required recurrent oral ulcers for BD diagnosis, whereas the 2014 International Criteria for BD improved sensitivity through a point-based system.<sup>1</sup>

The Journal of Rheumatology
Technion – Israel Institute of Technology (IL), Emek Medical Center (IL), Rambam Health Care Campus (IL)
Openalex Percentile: Top 51%
Otitis Media and Relapsing Polychondritis
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