Systematic review of clinical literature for absent common carotid artery

We recommend diagnostic head imaging to detect intracranial aneurysm in adult patients found to have ACCA and hypoplasia or tortuosity of the ipsilateral ICA. We also recommend carotid revascularization in patients found to have severe stenosis of the ipsilateral ICA, and this can safely be performed with open or endovascular methods. Current ACCA case report literature is of low quality and would benefit from improved reporting of patient demographics and clinical management strategies.