Long-term outcomes and prognostic predictors in patients with fibrosing mediastinitis associated pulmonary hypertension: a multicenter cohort study

Although the 1-, 3-, and 5-year overall survival rates were relatively favorable, the 5-year clinical worsening-free rate was not satisfying. Elevated hs-CRP, mPAP and the presence of peripheral edema were independently associated with worse clinical outcomes.

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Publication Details

Journal
Orphanet Journal of Rare Diseases
Published
2025-11-12
DOI
https://doi.org/10.1186/s13023-025-04066-8
Citations
1
Primary Topic
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
Type
article
Field-Weighted Citation Impact
1.52
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article

Long-term outcomes and prognostic predictors in patients with fibrosing mediastinitis associated pulmonary hypertension: a multicenter cohort study

Yu Tang, Wenjie Yan, Hongyun Ruan, Xiaoming Zhou et al.
1 citations
Orphanet Journal of Rare Diseases
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
1.52
article

Long-term outcomes and prognostic predictors in patients with fibrosing mediastinitis associated pulmonary hypertension: a multicenter cohort study

Yu Tang, Wenjie Yan, Hongyun Ruan, Xiaoming Zhou, Lingyan You, Beilan Yang, Gaxue Jiang, Yinli Wang, Yan Wu, Yicheng Yang, Yanru Liang, Qixian Zeng, Qunying Xi, Hanwen Zhang, Zhihong Liu, Ting Wang, Qin Luo, Yu Chen, Zhihui Zhao, Bingyang Liu, Jinglong Nan, Changming Xiong, Xincao Tao, Tao Yang
article en
1 citations

Abstract

Although the 1-, 3-, and 5-year overall survival rates were relatively favorable, the 5-year clinical worsening-free rate was not satisfying. Elevated hs-CRP, mPAP and the presence of peripheral edema were independently associated with worse clinical outcomes.

Orphanet Journal of Rare DiseasesVol. 20(1)
Chinese Academy of Medical Sciences & Peking Union Medical College (CN), Kunming Medical University (CN), Third People's Hospital of Chengdu (CN), Inner Mongolia People's Hospital (CN), Xuzhou Central Hospital (CN), Fu Wai Hospital (CN), First Hospital of Lanzhou University (CN), Lanzhou University (CN)
Openalex Percentile: Top 13%
Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
1.52
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