Long-term outcomes and prognostic predictors in patients with fibrosing mediastinitis associated pulmonary hypertension: a multicenter cohort study
Although the 1-, 3-, and 5-year overall survival rates were relatively favorable, the 5-year clinical worsening-free rate was not satisfying. Elevated hs-CRP, mPAP and the presence of peripheral edema were independently associated with worse clinical outcomes.
Authors
- Yu Tang (ORCID: https://orcid.org/0000-0002-7067-8066)
- Wenjie Yan
- Hongyun Ruan
- Xiaoming Zhou (ORCID: https://orcid.org/0000-0002-3240-9789)
- Lingyan You
- Beilan Yang
- Gaxue Jiang
- Yinli Wang (ORCID: https://orcid.org/0000-0003-2129-1225)
- Yan Wu (ORCID: https://orcid.org/0000-0002-2355-0887)
- Yicheng Yang (ORCID: https://orcid.org/0000-0003-2884-2341)
- Yanru Liang (ORCID: https://orcid.org/0000-0002-0283-4362)
- Qixian Zeng (ORCID: https://orcid.org/0000-0001-6855-995X)
- Qunying Xi (ORCID: https://orcid.org/0000-0003-1013-7775)
- Hanwen Zhang (ORCID: https://orcid.org/0000-0001-8955-7494)
- Zhihong Liu (ORCID: https://orcid.org/0000-0001-6093-0726)
- Ting Wang (ORCID: https://orcid.org/0000-0002-7787-1192)
- Qin Luo (ORCID: https://orcid.org/0000-0002-1351-7231)
- Yu Chen (ORCID: https://orcid.org/0000-0001-5238-8420)
- Zhihui Zhao (ORCID: https://orcid.org/0000-0002-2543-7984)
- Bingyang Liu
- Jinglong Nan
- Changming Xiong
- Xincao Tao
- Tao Yang (ORCID: https://orcid.org/0000-0002-7795-6081)
Institutions
- Chinese Academy of Medical Sciences & Peking Union Medical College (CN)
- Kunming Medical University (CN)
- Third People's Hospital of Chengdu (CN)
- Inner Mongolia People's Hospital (CN)
- Xuzhou Central Hospital (CN)
- Fu Wai Hospital (CN)
- First Hospital of Lanzhou University (CN)
- Lanzhou University (CN)
Publication Details
- Journal
- Orphanet Journal of Rare Diseases
- Published
- 2025-11-12
- DOI
- https://doi.org/10.1186/s13023-025-04066-8
- Citations
- 1
- Primary Topic
- Interstitial Lung Diseases and Idiopathic Pulmonary Fibrosis
- Type
- article
- Field-Weighted Citation Impact
- 1.52