Intravenous immunoglobulin and febrile status epilepticus in children with Dravet syndrome: A retrospective multicentre study
These series suggest a potential benefit of IVIG in reducing status epilepticus in selected children with Dravet syndrome. However, tolerability and feasibility issues were identified. A prospective controlled trial is warranted to further define the role of IVIG in this population.
Authors
- Nicole Chémaly (ORCID: https://orcid.org/0000-0002-2333-9408)
- Rima Nabbout (ORCID: https://orcid.org/0000-0001-5877-4074)
- Mathieu Kuchenbuch (ORCID: https://orcid.org/0000-0002-5944-2204)
- Claire Bar (ORCID: https://orcid.org/0000-0003-1489-0211)
- Sylviane Peudenier (ORCID: https://orcid.org/0000-0002-1463-1343)
- Hélène Maurey
- Sylvie Nguyen The Tich (ORCID: https://orcid.org/0000-0003-4836-0120)
- Caroline Espil‐Taris
- Elodie Lametery
- Romane Marc (ORCID: https://orcid.org/0009-0005-8088-2684)
Institutions
- Hôpital Necker-Enfants Malades (FR)
- Centre National de la Recherche Scientifique (FR)
- Université de Bordeaux (FR)
- Inserm (FR)
- Université Paris Cité (FR)
- Université de Lille (FR)
- Centre Hospitalier Universitaire de Grenoble (FR)
- Centre Hospitalier Universitaire de Bordeaux (FR)
- Centre Hospitalier Universitaire de Lille (FR)
- Centre Hospitalier Universitaire Amiens-Picardie (FR)
- Centre Hospitalier Régional et Universitaire de Nancy (FR)
- Ingénierie Moléculaire et Physiopathologie Articulaire (FR)
- Bicêtre Hospital (FR)
- Institut des Maladies Génétiques Imagine (FR)
- Université Grenoble Alpes (FR)
- Université de Lorraine (FR)
Publication Details
- Journal
- Developmental Medicine & Child Neurology
- Published
- 2025-11-12
- DOI
- https://doi.org/10.1111/dmcn.70077
- Primary Topic
- Epilepsy research and treatment
- Type
- article
- Field-Weighted Citation Impact
- 0.00