Posterior fossa decompression in syndromic children with chiari-like posterior fossa crowding: a nationwide US-based study
The syndromic Chiari-like condition is associated with distinct baseline characteristics and higher short-term complication rates following PFD compared to true CM1. While syndromic status was independently associated with reoperation, it was not an independent predictor of overall complications or readmissions. These findings suggest that patients with syndromes mimicking CM1 represent a clinically and etiologically distinct entity, warranting tailored management and further investigation.
Authors
- Victor E. Staartjes (ORCID: https://orcid.org/0000-0003-1039-2098)
- Erik Edström (ORCID: https://orcid.org/0000-0002-8781-1169)
- Pascal M. Jabbour (ORCID: https://orcid.org/0000-0002-8965-2413)
- Victor Gabriel El-Hajj (ORCID: https://orcid.org/0000-0001-9479-761X)
- Joanna M. Roy (ORCID: https://orcid.org/0000-0002-4829-1869)
- Maria Gharios (ORCID: https://orcid.org/0000-0002-3614-8782)
- Basel Musmar (ORCID: https://orcid.org/0009-0000-4910-6090)
- Adrian Elmi‐Terander (ORCID: https://orcid.org/0000-0002-3776-6136)
- Erik Öhlén
- Ihab Ahmad Al-Rikabi
- Josué Aganze Mwambali
Institutions
- Örebro University (SE)
- Thomas Jefferson University Hospital (US)
- Karolinska Institutet (SE)
- University Hospital of Zurich (CH)
- Université Catholique de Bukavu (CD)
Publication Details
- Journal
- Child s Nervous System
- Published
- 2025-11-11
- DOI
- https://doi.org/10.1007/s00381-025-06954-7
- Citations
- 1
- Primary Topic
- Spinal Dysraphism and Malformations
- Type
- article
- Field-Weighted Citation Impact
- 1.88