The importance of considering progression speed in systemic sclerosis—associated interstitial lung diseases: application of 2022 and 2024 clinical practice guidelines for progressive pulmonary fibrosis, a retrospective cohort study
Our findings suggest that short-term and slow progressions have distinct prognostic implications and may require dedicated therapeutic management.
Authors
- Pierre‐Yves Brillet (ORCID: https://orcid.org/0000-0002-2411-5545)
- Y. Uzunhan (ORCID: https://orcid.org/0000-0002-1607-1407)
- F. Caux (ORCID: https://orcid.org/0000-0001-9552-0882)
- Stéphane Tran Ba
- Anaïs Roeser (ORCID: https://orcid.org/0000-0001-6717-3115)
- Hilario Nunès (ORCID: https://orcid.org/0000-0003-2896-7347)
- Robin Dhôte (ORCID: https://orcid.org/0000-0001-9969-9947)
Institutions
- Inserm (FR)
- Sorbonne Université (FR)
- Université Sorbonne Paris Nord (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- Association pour la Recherche en Physiologie de l’Environnement (FR)
- Hôpital Avicenne (FR)
Publication Details
- Journal
- Respiratory Research
- Published
- 2025-11-04
- DOI
- https://doi.org/10.1186/s12931-025-03375-7
- Citations
- 2
- Primary Topic
- Systemic Sclerosis and Related Diseases
- Type
- article
- Field-Weighted Citation Impact
- 2.94