Recurrent Intramuscular Hematoma Revealing Moderate Congenital Factor XIII Deficiency

Severe congenital factor XIII deficiency is a rare blood coagulation disorder that poses a risk of life-threatening bleeding complications. Conversely, patients with mild or moderate factor XIII deficiency frequently exhibit delayed or provoked bleeding patterns. This case report presents a patient who received a delayed diagnosis of moderate factor XIII deficiency following significant bleeding episodes in the postoperative period. We will examine the symptoms indicative of mild and moderate factor XIII deficiency, as well as the current therapeutic options. This discussion emphasizes the vital importance of early diagnosis for achieving optimal management and improved patient outcomes.

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Publication Details

Journal
Cureus
Published
2025-10-31
DOI
https://doi.org/10.7759/cureus.95841
Primary Topic
Blood properties and coagulation
Type
article
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article

Recurrent Intramuscular Hematoma Revealing Moderate Congenital Factor XIII Deficiency

Salma Riahi, Amina Bouatay, Nada Ben Halima, Imen Mgarrech et al.
Cureus
Blood properties and coagulation
article

Recurrent Intramuscular Hematoma Revealing Moderate Congenital Factor XIII Deficiency

Salma Riahi, Amina Bouatay, Nada Ben Halima, Imen Mgarrech, Ines Mazlout
article en

Abstract

Severe congenital factor XIII deficiency is a rare blood coagulation disorder that poses a risk of life-threatening bleeding complications. Conversely, patients with mild or moderate factor XIII deficiency frequently exhibit delayed or provoked bleeding patterns. This case report presents a patient who received a delayed diagnosis of moderate factor XIII deficiency following significant bleeding episodes in the postoperative period. We will examine the symptoms indicative of mild and moderate factor XIII deficiency, as well as the current therapeutic options. This discussion emphasizes the vital importance of early diagnosis for achieving optimal management and improved patient outcomes.

CureusVol. 17(10)
University of Monastir (TN), Hôpital Sahloul (TN), University of Sousse (TN)
Openalex Percentile: Top 54%
Blood properties and coagulation
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