Recurrent Intramuscular Hematoma Revealing Moderate Congenital Factor XIII Deficiency
Severe congenital factor XIII deficiency is a rare blood coagulation disorder that poses a risk of life-threatening bleeding complications. Conversely, patients with mild or moderate factor XIII deficiency frequently exhibit delayed or provoked bleeding patterns. This case report presents a patient who received a delayed diagnosis of moderate factor XIII deficiency following significant bleeding episodes in the postoperative period. We will examine the symptoms indicative of mild and moderate factor XIII deficiency, as well as the current therapeutic options. This discussion emphasizes the vital importance of early diagnosis for achieving optimal management and improved patient outcomes.
Authors
- Salma Riahi (ORCID: https://orcid.org/0009-0006-6398-1610)
- Amina Bouatay
- Nada Ben Halima
- Imen Mgarrech
- Ines Mazlout
Institutions
- University of Monastir (TN)
- Hôpital Sahloul (TN)
- University of Sousse (TN)
Publication Details
- Journal
- Cureus
- Published
- 2025-10-31
- DOI
- https://doi.org/10.7759/cureus.95841
- Primary Topic
- Blood properties and coagulation
- Type
- article
- Field-Weighted Citation Impact
- 0.00