The Silent Threat: Long QT Syndrome and the Shadow of Sudden Death

Case RepoRtWe conducted genetic testing for LQTS; the child was started on beta ()-blockers and mexiletine as the initial treatment.It was decided to tackle this situation by reducing cardiac sympathetic drive through bilateral thoracic cardiac sympathetic denervation.In this surgery, bilateral T1-T4 sympathetic ganglia were excised (Fig. 2), including the nerve of Kuntz.The postoperative recovery was uneventful, and the patient was continued on -blockers and mexiletine before being discharged in a hemodynamically stable condition.The genetic testing revealed a mutation of SCN5A gene, suggesting long QT3 syndrome.