A Unique Case of Pure Bilateral Lambdoid Craniosynostosis and Progression to Mercedes-Benz Syndrome Following Spring Cranioplasty
We report a case of a 3-month-old female with isolated bilateral lambdoid craniosynostosis treated by suturectomy with cranial springs, who later demonstrated unexpected sagittal fusion. The patient presented with bilateral lambdoid and mendosal fusion producing a distinctive posterior vault deformity. Springs placed at suturectomy were removed five months later. Segmented CT analysis revealed intracranial volume expansion from 727.4 cm<sup>3</sup> pre-op to 1371.9 cm<sup>3</sup> post-removal, with minimal blood loss and uncomplicated recovery. Post-removal imaging showed complete sagittal synostosis, suggesting either a delayed manifestation of Mercedes-Benz pattern synostosis or a mechanically induced secondary synostosis due to springs, warranting further investigation.
Authors
- Sarah A. Frommer (ORCID: https://orcid.org/0009-0009-7780-8394)
- Elizabeth C. Tyler‐Kabara (ORCID: https://orcid.org/0000-0003-3286-1094)
- Sebastian Kuriakose (ORCID: https://orcid.org/0009-0005-3586-3732)
- Patrick Kelley
- Yasmine Soubra
Institutions
- Dell Children's Medical Center of Central Texas (US)
- The University of Texas at Austin (US)
- Texas A&M University (US)
- Bryan College (US)
Publication Details
- Journal
- The Cleft Palate-Craniofacial Journal
- Published
- 2025-10-25
- DOI
- https://doi.org/10.1177/10556656251389537
- Primary Topic
- Craniofacial Disorders and Treatments
- Type
- article
- Field-Weighted Citation Impact
- 0.00