Unravelling IPAF, VEDOSS and connective tissue diseases classifications through the mixed connective tissue disease spectrum
At MCTD diagnosis, fulfilment of IPAF and/or VEDOSS criteria was not predictive of evolution toward SSc, whereas antiphospholipid antibodies and low C3 and/or C4 were predictive of an evolution toward SLE. This suggests that MCTD patients should be excluded from IPAF and VEDOSS.
Authors
- Kévin Chevalier (ORCID: https://orcid.org/0000-0001-7823-1827)
- Thomas Hanslik (ORCID: https://orcid.org/0000-0002-8670-7853)
- Cécile Goujard (ORCID: https://orcid.org/0000-0002-7956-0822)
- T. Papo (ORCID: https://orcid.org/0000-0002-7481-5099)
- Bertrand Dunogué (ORCID: https://orcid.org/0000-0003-2470-6166)
- Maxime Samson (ORCID: https://orcid.org/0000-0002-6547-232X)
- Jean‐Emmanuel Kahn (ORCID: https://orcid.org/0000-0002-9565-6074)
- Benjamin Thoreau (ORCID: https://orcid.org/0000-0002-9046-4524)
- Isabelle Koné‐Paut (ORCID: https://orcid.org/0000-0001-8939-5763)
- P. Cacoub (ORCID: https://orcid.org/0000-0002-6727-4992)
- H. Lévesque (ORCID: https://orcid.org/0000-0002-8133-3354)
- Alexis Régent (ORCID: https://orcid.org/0000-0002-8136-2454)
- Xavier Mariette (ORCID: https://orcid.org/0000-0002-4244-5417)
- Karim Sacré (ORCID: https://orcid.org/0000-0002-6544-234X)
- C. Agard
- Benjamin Chaigne (ORCID: https://orcid.org/0000-0001-5448-7860)
- Y. Benhamou (ORCID: https://orcid.org/0000-0001-8890-7341)
- N. Costedoat‐Chalumeau (ORCID: https://orcid.org/0000-0002-1555-9021)
- P. Duhaut (ORCID: https://orcid.org/0000-0002-1839-703X)
- Raphaèle Séror (ORCID: https://orcid.org/0000-0002-5523-1856)
- Félix Ackermann (ORCID: https://orcid.org/0000-0001-7209-4892)
- Marc Michel (ORCID: https://orcid.org/0000-0001-6613-8027)
- Véronique Le Guern
- Luc Mouthon (ORCID: https://orcid.org/0000-0002-7021-9492)
- Benjamin Terrier (ORCID: https://orcid.org/0000-0001-6612-7336)
- Bernard Bonnotte (ORCID: https://orcid.org/0000-0001-7229-3808)
- Jean M. Schmidt
- Brigitte Bader-Meunier
- Eric Hachulla
- Bertrand Godeau
- Pascal Cohen
- O. Lambotte
Institutions
- Hôpital Necker-Enfants Malades (FR)
- Université Paris Cité (FR)
- Université de Lille (FR)
- Université Paris-Saclay (FR)
- Centre Hospitalier Universitaire de Nantes (FR)
- Sorbonne Université (FR)
- Lille’s Cardiology Hospital (FR)
- Centre Hospitalier Universitaire de Tours (FR)
- Centre Hospitalier Universitaire Amiens-Picardie (FR)
- Assistance Publique – Hôpitaux de Paris (FR)
- CHU Dijon Bourgogne (FR)
- Pitié-Salpêtrière Hospital (FR)
- Centre d'Immunologie et des Maladies Infectieuses (FR)
- Hôpitaux Universitaires Henri-Mondor (FR)
- Hôpital Ambroise-Paré (FR)
- Hôpital Bichat-Claude-Bernard (FR)
- Centre Hospitalier Universitaire de Rouen (FR)
- Hôpital Foch (FR)
- Bicêtre Hospital (FR)
- Université de Rouen Normandie (FR)
Publication Details
- Journal
- RMD Open
- Published
- 2025-10-01
- DOI
- https://doi.org/10.1136/rmdopen-2025-006145
- Primary Topic
- Systemic Sclerosis and Related Diseases
- Type
- article
- Field-Weighted Citation Impact
- 0.00